Trombotik trombositopenik purpura

Ali Rıza ODABAŞ, Ramazan ÇETİNKAYA, Yılmaz SELÇUK
490 168

Öz


Trombotik trombositopenik purpura (TTP); mikroanjiyopatik hemolitik anemi, trombositopeni, değişken derecede nörolojik bozukluklar, ateş ve böbrek yetmezliği ile seyreden bir hastalıktır, Hastalıkta tipik patolojik lezyonlar küçük arteriollerde gelişen hyalin oklüzyonlardır. Hastalığın erken tanınması ve tedaviye başlanması yüksek mortalitesi olan bu hastalık için önemlidir. Bu makalede iki vaka nedeniyle TTP; klinik ve laboratuvar özellikleri, tanısı ve tedavisi bakımından literatür eşliğinde tartışılmıştır.

Anahtar kelimeler


Olgu sunumu,Purpura, trombotik trombositopenik,Tanı,Tedavi sonucu

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Referanslar


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